Adult Congenital Heart Disease 1st Edition by Sara Thorne, Sarah Bowater 0191078247 9780191078248

Part 1 Introduction to adult congenital heart disease

1 Epidemiology of ACHD

Introduction

Reasons for increased survival

Cause of death in ACHD

2 Morphology and classification

Introduction

Physiological classification

Sequential segmental analysis

Atrial arrangement

3 Non-invasive imaging

Introduction

Chest X-ray (CXR)

Transthoracic echocardiography (TTE)

Transoesophageal echo (TOE)

Cardiovascular magnetic resonance (CMR) imaging

Computed tomography (CT)

4 Physiological testing

Physiological testing

Types of exercise tests

Cardiopulmonary exercise testing

5 Cardiac catheterization

Introduction

Indications for cardiac catheterization

Precatheterization care

Normal values

Calculations

Catheter interventions in ACHD

6 Influence of pulmonary blood flow on management and outcome

Introduction

Pulmonary vascular development in early life

Cyanotic heart disease and pulmonary blood flow

7 Cyanosis

Introduction

Examples of cyanotic congenital defects

Non-cardiac manifestations of cyanosis

Checklist for inpatients with cyanotic heart disease

Management of common emergencies in cyanotic heart disease

Part 2 Specific lesions

8 Valve and outflow tract lesions

Left ventricular outflow tract obstruction (LVOTO)

Left ventricular inflow lesions

Right ventricular outflow tract obstruction (RVOTO)

Ebstein anomaly

9 Septal defects

Atrial septal defects

Ventricular septal defects (VSDs)

Atrioventricular septal defects (AVSDs)

10 Eisenmenger syndrome

Introduction

Natural history

Complications and extracardiac manifestations

Physical signs

Investigations

Management

11 Aortic lesions

Introduction

Coarctation of the aorta

Patent ductus arteriosus (PDA)

Aortopulmonary window

Common arterial trunk/truncus arteriosus

Marfan syndrome

Loeys Dietz syndrome

12 Venous anomalies

Anomalies of systemic venous drainage

Anomalies of pulmonary venous drainage

13 Transposition complexes

Introduction

Complete transposition of the great arteries (TGA)

Congenitally corrected TGA (ccTGA)

14 Tetralogy of Fallot and pulmonary atresia with VSD

Tetralogy of Fallot

Natural (unoperated) or shunt-palliated history

Operated history—follow-up after radical repair

Pulmonary atresia with VSD

15 Functionally univentricular hearts and Fontan circulation

The functionally univentricular heart

Staged approach to achieve definitive palliation

Fontan circulation

Hypoplastic left heart syndrome

16 Pulmonary hypertension in ACHD

Introduction

Classification

Investigations

Management

17 Rare conditions presenting in adulthood

Coronary anomalies

Sinus of Valsalva aneurysm

Part 3 General management issues of adult congenital heart disease

18 Emergencies

Introduction

Haemoptysis in a cyanotic patient

Other emergencies and pitfalls to avoid in cyanotic heart disease

Haemoptysis or haematemesis in patient with repaired coarctation

Tachyarrhythmias

19 Heart failure in ACHD

Introduction

Drug therapy

Transplantation in ACHD

End-of-life care in ACHD

20 Device therapy in ACHD

Introduction

Bradycardia pacing

Implantable cardiac defibrillators (ICDs)

Cardiac resynchronization therapy (CRT)

Technical considerations

21 Contraception and pregnancy

Introduction

General principles

Contraception

Preconception

Pregnancy and delivery

Post-partum

22 Endocarditis

Endocarditis prophylaxis

23 Transition and transfer of care

Transition and transfer of care

24 Lifestyle issues

Exercise

Diving

Travel

Insurance

Glossary of terms

Appendix 1

Appendix 2

Appendix 3

Index